Cleidocranial dysplasia: 2 generations of management.

نویسندگان

  • John Daskalogiannakis
  • Luis Piedade
  • Tom C Lindholm
  • George K B Sándor
  • Robert P Carmichael
چکیده

Patients with cleidocranial dysplasia (CCD) commonly present with significant dental problems, such as retention of multiple deciduous teeth, impaction or delay in eruption of permanent teeth and, often, the presence of supernumerary teeth. Several approaches have been described for the management of such patients. We report 2 cases illustrating the shift in the management paradigm from edentulation and prosthetic replacement to orthodontically assisted forced eruption and fixed appliance orthodontic treatment combined with orthognathic surgery.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Familial Cleidocranial Dysplasia in a Neonate: A Case Report

Background: Cleidocranial dysplasia (CCD) is a rare inherited skeletal dysplasia, with an incidence of 1 case per 1000,000 individuals. It is a form of predominantly autosomal dominant inheritance and is associated with a mutation in runt related transcription factor-2 gene mapped on chromosome 6p21. This disease primarily affects the bones formed by intramembranous ossification and is characte...

متن کامل

Anesthetic management during a cesarean section in a patient with cleidocranial dysplasia: a case report

Background Cleidocranial dysplasia is a type of skeletal dysplasia, which is primarily characterized by delayed ossification of skeletal structures. It causes facial and oral abnormalities, resulting in difficult airway management and neuraxial anesthesia. Case presentation The patient was a 24-year-old primipara (height 138 cm, weight 42 kg) with a hypoplastic right clavicle, patent fontanel...

متن کامل

Cleidocranial Dysplasia Sudersan et al

Cleidocranial dysplasia is a autosomal dominant inherited disorder, and it is the primary disorder of the bone. When the clinicians’ suspect this syndrome, they check for the presence of clavicles. In the literature, yet several other features are reported. Several researches including Chromosomal studies and dermatoglyphics are carried out, for the prevention and management strategies’. This r...

متن کامل

Abstract # 231: Anaesthetic Management of a Primigravida Patient with Cleidocranial Dysplasia Undergoing Caesarean Section

231 Anaesthetic Management of a Primigravida Patient with Cleidocranial Dysplasia Undergoing Caesarean Section Abstract Type: Case Report/Case Series Yat W Li, B.Sc. Biochemistry, B.M. Medicine, FRCA; Awini Gunasekera, B.Sc., M.B., B.S., M.R.C.P., FRCA; Garud S. Chandan, M.B., B.S., FRCA Mid Staffordshire NHS Foundation TrustType: Case Report/Case Series Yat W Li, B.Sc. Biochemistry, B.M. Medic...

متن کامل

Cleidocranial Dysplasia: A Clinico-radiographic Spectrum with Differential Diagnosis

INTRODUCTION Cleidocranial dysplasia (CCD) is characterized by aplasia or hypoplasia of the clavicles, characteristic craniofacial malformations, and the presence of numerous supernumerary and unerupted teeth. It affects bones derived from both intra-membranous and endochondral ossification. Incidence has been reported as 1 in 10,00,000. It is caused by mutation in the gene encoding transcripti...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • Journal

دوره 72 4  شماره 

صفحات  -

تاریخ انتشار 2006